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Employment (6)

University of Oulu: Oulu, FI

2022-09-01 to present | University Researcher (Faculty of Biochemistry and Molecular Medicine)
Employment
Source: Self-asserted source
Kaija Autio

University of Oulu: Oulu, FI

2017-08-01 to 2022-08-31 | Researcher and line manager (Faculty of Biochemistry and Molecular Medicine)
Employment
Source: Self-asserted source
Kaija Autio

University of Oulu: Oulu, FI

2016-09-01 to 2017-07-31 | Academy of Finland Postdoctoral Researcher (Faculty of Biochemistry and Molecular Medicine)
Employment
Source: Self-asserted source
Kaija Autio

The University of Arizona: Tucson, AZ, US

2015-09-01 to 2016-08-31 | Academy of Finland Postdoctoral Researcher (Department of Molecular And Cellular Biology)
Employment
Source: Self-asserted source
Kaija Autio

University of Oulu: Oulu, FI

2013-09-01 to 2015-08-31 | Academy of Finland Postdoctoral Researcher (Faculty of Biochemistry and Molecular Medicine)
Employment
Source: Self-asserted source
Kaija Autio

University of Oulu: Oulu, FI

2008-01-01 to 2013-08-31 | Postdoctoral Researcher (Department of Biochemistry)
Employment
Source: Self-asserted source
Kaija Autio

Education and qualifications (3)

University of Oulu: Oulu, FI

2020 to present | Docent in Medical Biochemistry and Molecular Biology (Faculty of Biochemistry and Molecular Medicine)
Qualification
Source: Self-asserted source
Kaija Autio

University of Oulu: Oulu, FI

2001-01-01 to 2007-12-21 | PhD (Department of Biochemistry)
Education
Source: Self-asserted source
Kaija Autio

University of Oulu: Oulu, FI

1995 to 2000-12-12 | MSc (Department of Biochemistry)
Education
Source: Self-asserted source
Kaija Autio

Funding (6)

Mitokondriaaliseen enoyyli-CoA reduktaasiin liittyvä näköhermon surkastuminen – kohti geenihoitoja

2024 to 2026 | Grant
Mary och Georg C. Ehrnrooths Stiftelse (Helsinki, FI)
Source: Self-asserted source
Kaija Autio

Mitokondriaaliseen enoyyli-CoA reduktaasiin liittyvä näköhermon surkastuminen – kohti geenihoitoja

2023-09 to 2024-08 | Grant
Mary och Georg C. Ehrnrooths Stiftelse (Helsinki, FI)
Source: Self-asserted source
Kaija Autio

Mitokondriaaliseen enoyyli-CoA-reduktaasiin liittyvä näköhermon surkastuminen

2022-09 to 2023-08 | Grant
Mary och Georg C. Ehrnrooths Stiftelse (Helsinki, FI)
Source: Self-asserted source
Kaija Autio

Mitochondrial fatty acid synthesis in nutritional state signaling and human disorders

2022-05 to 2025-04 | Grant
Sigrid Jusélius Foundation (Helsinki, FI)
Source: Self-asserted source
Kaija Autio

Mitokondriaaliseen enoyyli-CoA-reduktaasiin liittyvä näköhermon surkastuminen

2021-06 to 2022-05 | Grant
Mary and Georg C. Ehrnrooth Foundation (Helsinki, FI)
Source: Self-asserted source
Kaija Autio

Novel circuit controlling cell metabolism - tetrahydrofolate, C1-fragments and lipid biosynthesis

2013-09 to 2017-07 | Grant
Academy of Finland (Helsinki, FI)
Source: Self-asserted source
Kaija Autio

Works (25)

Biallelic Variants in LIPT2 as a Cause of Infantile-Onset Dystonia: Expanding the Clinical and Molecular Spectrum

Pediatric Neurology
2025-01 | Journal article
Contributors: Kuntal Sen; Alonso Zea Vera; Anna Puronurmi; Andrea Gropman; Parith Wongkittichote; Rebecca Ganetzky; Kaija Autio; Alexander Kastaniotis
Source: check_circle
Crossref

Exploration of dietary interventions to treat mitochondrial fatty acid disorders in a mouse model

The Journal of Nutritional Biochemistry
2024-09 | Journal article
Contributors: Kaija J. Autio; Hennariikka Koivisto; Werner Schmitz; Anna Puronurmi; Heikki Tanila; Alexander J. Kastaniotis
Source: check_circle
Crossref

Biallelic Variants in LIPT2 as a Cause of Infantile-Onset Dystonia: Expanding the Clinical and Molecular Spectrum

Preprints.org
2024-05-09 | Preprint
Contributors: Kaija Autio
Source: Self-asserted source
Kaija Autio

An engineered variant of MECR reductase reveals indispensability of long-chain acyl-ACPs for mitochondrial respiration

Nature Communications
2023-02-04 | Journal article | Author
Part of ISSN: 2041-1723
Contributors: Mohammad Tanvir Rahman; M. Kristian Koski; Joanna Panecka-Hofman; Werner Schmitz; Alexander J. Kastaniotis; Rebecca Wade; rik wierenga; J Kalervo Hiltunen; Kaija Autio
Source: Self-asserted source
Kaija Autio
grade
Preferred source (of 2)‎

Expression and analysis of the SAM-dependent RNA methyltransferase Rsm22 from Saccharomyces cerevisiae.

Acta crystallographica. Section D, Structural biology
2021-05-19 | Journal article
Source: Self-asserted source
Kaija Autio
grade
Preferred source (of 2)‎

Mitochondrial Fatty Acids and Neurodegenerative Disorders.

The Neuroscientist : a review journal bringing neurobiology, neurology and psychiatry
2020-07 | Journal article
Contributors: Kastaniotis AJ; Autio KJ; R Nair R
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Binding of Brucella protein, Bp26, to select extracellular matrix molecules.

BMC molecular and cell biology
2019-11 | Journal article
Contributors: ElTahir Y; Al-Araimi A; Nair RR; Autio KJ; Tu H; Leo JC; Al-Marzooqi W; Johnson EH
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

CoA-dependent activation of mitochondrial acyl carrier protein links four neurodegenerative diseases.

EMBO molecular medicine
2019-11 | Journal article
Contributors: Lambrechts RA; Schepers H; Yu Y; van der Zwaag M; Autio KJ; Vieira-Lara MA; Bakker BM; Tijssen MA; Hayflick SJ; Grzeschik NA et al.
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Mitochondrial 2,4-dienoyl-CoA reductase (Decr) deficiency and impairment of thermogenesis in mouse brown adipose tissue.

Scientific reports
2019-08 | Journal article
Contributors: Mäkelä AM; Hohtola E; Miinalainen IJ; Autio JA; Schmitz W; Niemi KJ; Hiltunen JK; Autio KJ
Source: Self-asserted source
Kaija Autio via Europe PubMed Central
grade
Preferred source (of 2)‎

Mitochondrial acyl carrier protein (ACP) at the interface of metabolic state sensing and mitochondrial function.

Biochimica et biophysica acta. Molecular cell research
2019-08 | Journal article
Contributors: Masud AJ; Kastaniotis AJ; Rahman MT; Autio KJ; Hiltunen JK
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

17B-hydroxysteroid dehydrogenases as acyl thioester metabolizing enzymes.

Molecular and cellular endocrinology
2018-11 | Journal article
Contributors: Hiltunen JK; Kastaniotis AJ; Autio KJ; Jiang G; Chen Z; Glumoff T
Source: Self-asserted source
Kaija Autio via Europe PubMed Central
grade
Preferred source (of 2)‎

Impaired Mitochondrial Fatty Acid Synthesis Leads to Neurodegeneration in Mice.

The Journal of neuroscience : the official journal of the Society for Neuroscience
2018-09 | Journal article
Contributors: Nair RR; Koivisto H; Jokivarsi K; Miinalainen IJ; Autio KJ; Manninen A; Poutiainen P; Tanila H; Hiltunen JK; Kastaniotis AJ
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Genetic modifications of Mecr reveal a role for mitochondrial 2-enoyl-CoA/ACP reductase in placental development in mice.

Human molecular genetics
2017-06 | Journal article
Contributors: Nair RR; Kerätär JM; Autio KJ; Masud AJ; Finnilä MAJ; Autio-Harmainen HI; Miinalainen IJ; Nieminen PA; Hiltunen JK; Kastaniotis AJ
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Odd Chain Fatty Acids; New Insights of the Relationship Between the Gut Microbiota, Dietary Intake, Biosynthesis and Glucose Intolerance.

Scientific reports
2017-03 | Journal article
Contributors: Jenkins BJ; Seyssel K; Chiu S; Pan PH; Lin SY; Stanley E; Ament Z; West JA; Summerhill K; Griffin JL et al.
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Mitochondrial fatty acid synthesis, fatty acids and mitochondrial physiology.

Biochimica et biophysica acta. Molecular and cell biology of lipids
2016-08 | Journal article
Contributors: Kastaniotis AJ; Autio KJ; Kerätär JM; Monteuuis G; Mäkelä AM; Nair RR; Pietikäinen LP; Shvetsova A; Chen Z; Hiltunen JK
Source: Self-asserted source
Kaija Autio via Europe PubMed Central
grade
Preferred source (of 2)‎

Phytol is lethal for Amacr-deficient mice.

Biochimica et biophysica acta
2015-08 | Journal article
Contributors: Selkälä EM; Nair RR; Schmitz W; Kvist AP; Baes M; Hiltunen JK; Autio KJ
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Role of AMACR (α-methylacyl-CoA racemase) and MFE-1 (peroxisomal multifunctional enzyme-1) in bile acid synthesis in mice.

The Biochemical journal
2014-07 | Journal article
Contributors: Autio KJ; Schmitz W; Nair RR; Selkälä EM; Sormunen RT; Miinalainen IJ; Crick PJ; Wang Y; Griffiths WJ; Reddy JK et al.
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Metabolic adaptation allows Amacr-deficient mice to remain symptom-free despite low levels of mature bile acids.

Biochimica et biophysica acta
2013-05 | Journal article
Contributors: Selkälä EM; Kuusisto SM; Salonurmi T; Savolainen MJ; Jauhiainen M; Pirilä PL; Kvist AP; Conzelmann E; Schmitz W; Alexson SE et al.
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Mitochondrial fatty acid synthesis and respiration.

Biochimica et biophysica acta
2010-03 | Journal article
Contributors: Hiltunen JK; Autio KJ; Schonauer MS; Kursu VA; Dieckmann CL; Kastaniotis AJ
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Mitochondrial 2,4-dienoyl-CoA reductase deficiency in mice results in severe hypoglycemia with stress intolerance and unimpaired ketogenesis.

PLoS genetics
2009-07 | Journal article
Contributors: Miinalainen IJ; Schmitz W; Huotari A; Autio KJ; Soininen R; Ver Loren van Themaat E; Baes M; Herzig KH; Conzelmann E; Hiltunen JK
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Mitochondrial fatty acid synthesis type II: more than just fatty acids.

The Journal of biological chemistry
2008-11 | Journal article
Contributors: Hiltunen JK; Schonauer MS; Autio KJ; Mittelmeier TM; Kastaniotis AJ; Dieckmann CL
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

The 3-hydroxyacyl-ACP dehydratase of mitochondrial fatty acid synthesis in Trypanosoma brucei.

FEBS letters
2008-02 | Journal article
Contributors: Autio KJ; Guler JL; Kastaniotis AJ; Englund PT; Hiltunen JK
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

An ancient genetic link between vertebrate mitochondrial fatty acid synthesis and RNA processing.

FASEB journal : official publication of the Federation of American Societies for Experimental Biology
2007-09 | Journal article
Contributors: Autio KJ; Kastaniotis AJ; Pospiech H; Miinalainen IJ; Schonauer MS; Dieckmann CL; Hiltunen JK
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Mitochondrial fatty acid synthesis and maintenance of respiratory competent mitochondria in yeast.

Biochemical Society transactions
2005-11 | Journal article
Contributors: Hiltunen JK; Okubo F; Kursu VA; Autio KJ; Kastaniotis AJ
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Htd2p/Yhr067p is a yeast 3-hydroxyacyl-ACP dehydratase essential for mitochondrial function and morphology.

Molecular microbiology
2004-09 | Journal article
Contributors: Kastaniotis AJ; Autio KJ; Sormunen RT; Hiltunen JK
Source: Self-asserted source
Kaija Autio via Europe PubMed Central

Peer review (1 review for 1 publication/grant)

Review activity for Nature metabolism. (1)